AnilBaranMukherjeeMD

PubMed

• 1 citations
  Ablation of microRNA-155 and neuroinflammation in a mouse model of CLN1-disease.
  Tamal Sadhukhan, Maria B. Bagh, Sriparna Sadhukhan, Abhilash P. Appu, Avisek Mondal, James R. Iiben, Tianwei Li, Steven L. Coon, Anil B. Mukherjee> ;Biochemical and Biophysical Research Communications. 2021 Sep 24
• 12 citations
  In a mouse model of INCL reduced S-palmitoylation of cytosolic thioesterase APT1 contributes to microglia proliferation and neuroinflammation.
  Tamal Sadhukhan, Maria B. Bagh, Abhilash P. Appu, Avisek Mondal, Wei Zhang, Aiyi Liu, Anil B. Mukherjee> ;Journal of Inherited Metabolic Disease. 2021 Mar 19
• 15 citations
  Cln1‐mutations suppress Rab7‐RILP interaction and impair autophagy contributing to neuropathology in a mouse model of infantile neuronal ceroid lipofuscinosis
  Chinmoy Sarkar, Tamal Sadhukhan, Maria B. Bagh, Abhilash P. Appu, Goutam Chandra, Avisek Mondal, Arjun Saha, Anil B. Mukherjee> ;Journal of Inherited Metabolic Disease. 2020 Apr 12
• 13 citations
  Cln3-mutations underlying juvenile neuronal ceroid lipofuscinosis cause significantly reduced levels of Palmitoyl-protein thioesterases-1 (Ppt1)-protein and Ppt1-enzym...
  Abhilash P. Appu, Maria B. Bagh, Tamal Sadhukhan, Avisek Mondal, Sydney Casey, Anil B. Mukherjee> ;Journal of Inherited Metabolic Disease. 2019 May 14
• 59 citations
  Emerging new roles of the lysosome and neuronal ceroid lipofuscinoses
  Anil B. Mukherjee, Abhilash P. Appu, Tamal Sadhukhan, Sydney Casey, Avisek Mondal, Zhongjian Zhang, Maria B. Bagh> ;Molecular Neurodegeneration. 2019 Jan 16
• 98 citations
  Misrouting of v-ATPase subunit V0a1 dysregulates lysosomal acidification in a neurodegenerative lysosomal storage disease model.
  Maria B. Bagh, Shiyong Peng, Goutam Chandra, Zhongjian Zhang, Satya P. Singh, Nagarajan Pattabiraman, Aiyi Liu, Anil B. Mukherjee> ;Nature Communications. 2017 Mar 7
• 18 citations
  MRI Brain Volume Measurements in Infantile Neuronal Ceroid Lipofuscinosis
  Eva H. Baker, Sondra W. Levin, Zhongjian Zhang, Anil B. Mukherjee> ;AJNR. American Journal of Neuroradiology. 2017 Feb 1
• 10 citations
  Suppression of agrin-22 production and synaptic dysfunction in Cln1-/- mice
  Shiyong Peng, Jianhua Xu, Kenneth A. Pelkey, Goutam Chandra, Zhongjian Zhang, Maria B. Bagh, Xiaoqing Yuan, Ling-Gang Wu, Chris J. McBain, Anil B. Mukherjee> ;Annals of Clinical and Translational Neurology. 2015 Dec 1
• 21 citations
  Cln1 gene disruption in mice reveals a common pathogenic link between two of the most lethal childhood neurodegenerative lysosomal storage disorders
  Goutam Chandra, Maria B. Bagh, Shiyong Peng, Arjun Saha, Chinmoy Sarkar, Matthew R Moralle, Zhongjian Zhang, Anil B. Mukherjee> ;Human Molecular Genetics. 2015 Oct 1
• 7 citations
  Evaluation of disease progression in INCL by MR spectroscopy.
  Eva H. Baker, Sondra W. Levin, Zhongjian Zhang, Anil B. Mukherjee> ;Annals of Clinical and Translational Neurology. 2015 Aug 1
• 18 citations
  Mice homozygous for c.451C>T mutation in Cln1 gene recapitulate INCL phenotype.
  Ashleigh Bouchelion, Zhongjian Zhang, Yichao Li, Haohua Qian, Anil B. Mukherjee> ;Annals of Clinical and Translational Neurology. 2014 Dec 1
• 49 citations
  Oral cysteamine bitartrate and N-acetylcysteine for patients with infantile neuronal ceroid lipofuscinosis: A pilot study
  Sondra W. Levin, Eva H. Baker, Wadih M. Zein, Zhongjian Zhang, Zenaide M.N. Quezado, Ning Miao, Andrea L. Gropman, Kurt J. Griffin, Simona Bianconi, Goutam Chandra, Om...> ;The Lancet. Neurology. 2014 Aug 1
• 53 citations
  Neuroprotection and lifespan extension in Ppt1 −/− mice by NtBuHA: therapeutic implications for INCL
  Chinmoy Sarkar, Goutam Chandra, Shiyong Peng, Zhongjian Zhang, Aiyi Liu, Anil B. Mukherjee> ;Nature Neuroscience. 2013 Nov 1
• 97 citations
  Dynamic Palmitoylation Links Cytosol-Membrane Shuttling of Acyl-protein Thioesterase-1 and Acyl-protein Thioesterase-2 with That of Proto-oncogene H-Ras Product and Gr...
  Eryan Kong, Shiyong Peng, Goutam Chandra, Chinmoy Sarkar, Zhongjian Zhang, Maria B. Bagh, Anil B. Mukherjee> ;The Journal of Biological Chemistry. 2013 Mar 29
• 11 citations
  In a model of Batten disease, palmitoyl protein thioesterase-1 deficiency is associated with brown adipose tissue and thermoregulation abnormalities.
  Alfia Khaibullina, Nicholas J. Kenyon, Virginia Guptill, Martha Quezado, Li Wang, Deloris E. Koziol, Robert Wesley, Pablo R. Moya, Zhongjian Zhang, Arjun Saha, Anil B....> ;Plos One. 2012 Nov 6
• 49 citations
  The blood-brain barrier is disrupted in a mouse model of infantile neuronal ceroid lipofuscinosis: amelioration by resveratrol
  Arjun Saha, Chinmoy Sarkar, Satya P. Singh, Zhongjian Zhang, Jeeva Munasinghe, Shiyong Peng, Goutam Chandra, Eryan Kong, Anil B. Mukherjee> ;Human Molecular Genetics. 2012 May 15
• 9 citations
  Evaluation of Neurodegeneration in a Mouse Model of Infantile Batten Disease by Magnetic Resonance Imaging and Magnetic Resonance Spectroscopy
  Jeeva Munasinghe, Zhongjian Zhang, Eryan Kong, Alison Heffer, Anil B. Mukherjee> ;Neuro-Degenerative Diseases. 2012 Feb 9
• 46 citations
  Stop codon read-through with PTC124 induces palmitoyl-protein thioesterase-1 activity, reduces thioester load and suppresses apoptosis in cultured cells from INCL pati...
  Chinmoy Sarkar, Zhongjian Zhang, Anil B. Mukherjee> ;Molecular Genetics and Metabolism. 2011 Nov 1
• 100 citations
  Allergic asthma: influence of genetic and environmental factors.
  Anil B. Mukherjee, Zhongjian Zhang> ;The Journal of Biological Chemistry. 2011 Sep 23
• 37 citations
  Disruption of adaptive energy metabolism and elevated ribosomal p-S6K1 levels contribute to INCL pathogenesis: partial rescue by resveratrol
  Hui Wei, Zhongjian Zhang, Arjun Saha, Shiyong Peng, Goutam Chandra, Zenaide M.N. Quezado, Anil B. Mukherjee> ;Human Molecular Genetics. 2011 Mar 15
• 35 citations
  Omega-3 and omega-6 fatty acids suppress ER- and oxidative-stress in cultured neurons and neuronal progenitor cells from mice lacking PPT1
  Sung-Jo Kim, Zhongjian Zhang, Arjun Saha, Chinmoy Sarkar, Zhenwen Zhao, Yan Xu, Anil B. Mukherjee> ;Neuroscience Letters. 2010 Aug 2
• 53 citations
  Lack of an Endogenous Anti-inflammatory Protein in Mice Enhances Colonization of B16F10 Melanoma Cells in the Lungs
  Arjun Saha, Yi-Ching Lee, Zhongjian Zhang, Goutam Chandra, Shao Bo Su, Anil B. Mukherjee> ;The Journal of Biological Chemistry. 2010 Apr 2
• 6 citations
  Subdural Fluid Collections in Patients With Infantile Neuronal Ceroid Lipofuscinosis
  Sondra W. Levin, Eva H. Baker, Andrea L. Gropman, Zenaide M.N. Quezado, Ning Miao, Zhongjian Zhang, Alice Jollands, Matteo Di Capua, Rafael C. Caruso, Anil B. Mukherjee> ;Archives of Neurology. 2009 Dec 1
• 17 citations
  Children with Infantile Neuronal Ceroid Lipofuscinosis Have an Increased Risk of Hypothermia and Bradycardia During Anesthesia
  Ning Miao, Sondra W. Levin, Eva H. Baker, Rafael C. Caruso, Zhongjian Zhang, Andrea L. Gropman, Deloris E. Koziol, Robert Wesley, Anil B. Mukherjee, Zenaide M.N. Quezado> ;Anesthesia and Analgesia. 2009 Aug 1
• 24 citations
  RAGE signaling contributes to neuroinflammation in infantile neuronal ceroid lipofuscinosis.
  Arjun Saha, Sung-Jo Kim, Zhongjian Zhang, Yi-Ching Lee, Chinmoy Sarkar, Pei-Chih Tsai, Anil B. Mukherjee> ;FEBS Letters. 2008 Nov 12
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